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Right bundle branch block and conduction disturbances in Brugada syndrome and arrhythmogenic right ventricular cardiomyopathy

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Journal of Interventional Cardiac Electrophysiology Aims and scope Submit manuscript

Abstract

Right bundle branch block is relatively frequent in the general population and is generally considered benign in healthy individuals. However, it has been associated with increased cardiovascular risk and all-cause mortality in various cohort studies. Indeed, the presence of right bundle branch block in subjects affected by cardiomyopathies or channelopathies is not rare and may conceal underlying electrocardiographic changes, thus making the diagnosis of such conditions more challenging. The purpose of this review is to analyze the prevalence and clinical significance of right bundle branch block in subjects affected by Brugada syndrome and arrhythmogenic right ventricular cardiomyopathy.

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Abbreviations

AC:

Arrhythmogenic cardiomyopathy

BrS:

Brugada syndrome

CMR:

Cardiac magnetic resonance

CRBBB:

Complete right bundle branch block

ECG:

Electrocardiogram

IRBBB:

Incomplete RBBB

IVF:

Idiopathic ventricular fibrillation

LV:

Left ventricle

RV:

Right ventricular

RVOT:

Right ventricular outflow tract

SAECG:

Signal averaged ECG

SCB:

Sodium channel blocker

TAD:

Terminal activation delay

TWI:

T wave inversion

SCD:

Sudden cardiac death

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Acknowledgements

We thank Margaret Knowles for the review of the English language.

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Authors and Affiliations

  1. Cardiology Division, Policlinico Casilino, Via Casilina 1049, 00169, Rome, Italy

    Leonardo Calò, Annamaria Martino & Ermenegildo de Ruvo

  2. Cardiology Department, Victor Babes University of Medicine and Pharmacy of Timisoara, Timișoara, Romania

    Emilia Goanta

  3. Cardiology Division, Nihon University School of Medicine, Tokyo, Japan

    Yasuo Okumura

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  1. Leonardo Calò
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  2. Annamaria Martino
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Correspondence to Leonardo Calò.

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Calò, L., Martino, A., Goanta, E. et al. Right bundle branch block and conduction disturbances in Brugada syndrome and arrhythmogenic right ventricular cardiomyopathy. J Interv Card Electrophysiol 52, 307–313 (2018). https://doi.org/10.1007/s10840-018-0386-3

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  • DOI: https://doi.org/10.1007/s10840-018-0386-3

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