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Congenital ectropion uveae presenting as acute glaucoma in a 3-year-old child

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Abstract

Congenital ectropion uveae is a rare anomaly commonly associated with neurofibromatosis and occasionally with other ocular abnormalities. Glaucoma related with this condition may be present in infancy, or may develop later in life, and is thought to be due to an associated angle dysgenesis. Diagnosis is frequently delayed due to the subtle signs and the absence of symptoms and management is primarily surgical. We report an unusual case of unilateral congenital ectropion uveae in a 3-year-old child, with no evidence of neurofibromatosis, presenting as acute glaucoma, which was successfully managed by topical treatment only, avoiding surgical intervention.

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Acknowledgements

This work was not supported by grants or funds, and there is no commercial or proprietary interest on any product or company.

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Authors and Affiliations

  1. 1st Department of Ophthalmology, Aristotle University of Thessaloniki, AHEPA Hospital, 3 Pl. Ippodromiou Street, 54621, Thessaloniki, Greece

    N. G. Ziakas, A. Chranioti, A. Malamas & O. Leliopoulou

  2. 2nd Department of Ophthalmology, Aristotle University of Thessaloniki, Papageorgiou Hospital, Thessaloniki, Greece

    A. Mataftsi

Authors
  1. N. G. Ziakas
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  2. A. Chranioti
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  3. A. Malamas
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  4. O. Leliopoulou
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  5. A. Mataftsi
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Correspondence to A. Chranioti.

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Ziakas, N.G., Chranioti, A., Malamas, A. et al. Congenital ectropion uveae presenting as acute glaucoma in a 3-year-old child. Int Ophthalmol 34, 97–98 (2014). https://doi.org/10.1007/s10792-013-9735-5

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  • DOI: https://doi.org/10.1007/s10792-013-9735-5

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