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Congenital iris ectropion associated with juvenile glaucoma

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Abstract

Congenital iris ectropion is an uncommon malformation of the anterior segment of the eye. The authors describe a case of bilateral congenital iris ectropion associated with juvenile glaucoma in an otherwise healthy 9-year-old girl. Intra-ocular pressure (IOP) measured by Goldmann applanation tonometry was 40 mmHg in the right eye and 32 mmHg in the left eye. Despite maximum IOP lowering therapy, the desired IOP levels needed to prevent further progression of the glaucoma could not be achieved. Visual field testing and confocal scanning laser tomography showed glaucomatous neuropathy. Trabeculectomy with antimetabolites (mitomycin C 0.2 mg/ml) was performed in both eyes and IOP was normalized without IOP lowering medications during a follow-up of 4 years. The authors point out the importance of recognizing congenital iris ectropion early to prevent blindness in young patients and improve their prognosis.

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Conflict of interest

The authors have no public or private financial support in this study. The authors have no financial or proprietary interest in any of the products, methods, or materials mentioned in this study.

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Correspondence to Göktuğ Seymenoğlu.

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The study was performed in Celal Bayar University Faculty of Medicine, Manisa, Turkey.

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Seymenoğlu, G., Başer, E. Congenital iris ectropion associated with juvenile glaucoma. Int Ophthalmol 31, 33–38 (2011). https://doi.org/10.1007/s10792-010-9388-6

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  • DOI: https://doi.org/10.1007/s10792-010-9388-6

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