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Branch retinal artery occlusion with visual field and multifocal erg in Susac syndrome: a case report

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Abstract

A 19-year-old woman presented with subacute encephalopathy and subsequently developed hearing loss and occlusions of branches of the central retinal artery. The triad of microangiopathy of the brain, retina and cochlea is typical for Susac syndrome. The etiology of this syndrome is still unknown, but the prognosis is good in most cases. Spontaneous resolution usually occurs, but early treatment minimizes the risk of sequelae. Multifocal ERG may be useful to assess subclinical retinal dysfunction after recovery of subjective symptoms of BRAO in Susac syndrome.

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Acknowledgments

We would like to thank Bert Verhelst for his devoted work in the electrophysiology department.

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Authors and Affiliations

  1. Departement Oogheelkunde, UZ Brussel, Vrije Universiteit Brussel, VUB, Laarbeeklaan 101, 1090, Jette, Belgium

    Marianne van Winden & Paul Salu

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  1. Marianne van Winden
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  2. Paul Salu
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Correspondence to Marianne van Winden.

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van Winden, M., Salu, P. Branch retinal artery occlusion with visual field and multifocal erg in Susac syndrome: a case report. Doc Ophthalmol 121, 223–229 (2010). https://doi.org/10.1007/s10633-010-9244-z

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  • DOI: https://doi.org/10.1007/s10633-010-9244-z

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