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Annular fundus autofluorescence abnormality in a case of macular dystrophy

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Abstract

Purpose: To present a case of macular dystrophy with early changes in fundus autofluorescence. Methods: A 20-year-old woman with a recent loss of visual acuity and onset of photophobia was examined. Color vision and visual field testing, fluorescein angiography, full-field and multifocal electroretinograms as well as fundus autofluorescence were performed. Results: Best-corrected visual acuity was 20/100 (right eye) and 20/60 (left eye). There was a red-green color vision defect and a relative central scotoma in both eyes. Ophthalmoscopy and fluorescein angiography were essentially normal, the presence of a dark choroid was debatable. Full-field ERG responses were normal, but the multifocal ERG showed severely reduced responses in the macular region. Both eyes showed a slight circular parafoveolar increase of fundus autofluorescence. Conclusion: Besides multifocal ERG, fundus autofluorescence aids to objectively assess the manifestation of macular dystrophies but does not discern between different types in early stages.

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Authors and Affiliations

  1. Department of Ophthalmology, University of Freiburg, Killianstr. 5, 79106, Freiburg, Germany

    Charlotte M. Poloschek, Lutz L. Hansen & Michael Bach

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  1. Charlotte M. Poloschek
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  2. Lutz L. Hansen
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  3. Michael Bach
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Correspondence to Charlotte M. Poloschek.

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Poloschek, C.M., Hansen, L.L. & Bach, M. Annular fundus autofluorescence abnormality in a case of macular dystrophy. Doc Ophthalmol 116, 91–95 (2008). https://doi.org/10.1007/s10633-007-9097-2

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  • DOI: https://doi.org/10.1007/s10633-007-9097-2

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