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Radiologic evaluation of coronary artery disease in adults with congenital heart disease

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Abstract

Improved surgical and medical therapy have prolonged survival in patients with congenital heart disease (CHD) such that general medical conditions like coronary artery disease (CAD) are now the main determinants of mortality. A summary of the association of CAD with CHD, as well as a discussion of the radiologic evaluation of the coronary arteries in adults with CHD is described herein. Cross sectional imaging to evaluate CAD in adults with CHD should follow the same appropriateness criteria as gender and aged matched patients without CHD. Coronary CT imaging may be particularly valuable in evaluating the coronary arteries in this patient population as invasive coronary angiography may prove challenging secondary to complicated or unconventional anatomy of the coronary arteries. Further, typical methods for evaluating CAD such as stress or echocardiography may be impractical in adults with CHD. Finally, delineating the anatomic relationship of the coronary arteries and their relationship with the sternum, chest wall, conduits, grafts, and valves is highly recommended in patients with CHD prior to reintervention to avoid iatrogenic complications.

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Authors and Affiliations

  1. Department of Radiology and Biomedical Imaging, University of California, San Francisco, 505 Parnassus Avenue, San Francisco, CA, 94143-0628, USA

    David M. Valenzuela & Karen G. Ordovas

Authors
  1. David M. Valenzuela
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  2. Karen G. Ordovas
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Correspondence to Karen G. Ordovas.

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The authors declare that they have no conflict of interest.

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Valenzuela, D.M., Ordovas, K.G. Radiologic evaluation of coronary artery disease in adults with congenital heart disease. Int J Cardiovasc Imaging 32, 13–18 (2016). https://doi.org/10.1007/s10554-015-0760-5

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  • DOI: https://doi.org/10.1007/s10554-015-0760-5

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