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Angeborene Fehlbildungen des unteren Respirationstraktes

Therapie und Langzeitmorbidität

Congenital malformations of the lower respiratory tract

Treatment and long-term morbidity

  • Leitthema
  • Published:
Der Pneumologe Aims and scope

Zusammenfassung

Dieser Beitrag gibt einen kurzen Überblick über die wichtigsten angeborenen Malformationen des unteren Respirationstraktes mit besonderer Betonung der Faktoren, die das Langzeitergebnis spezifischer Läsionen beeinflussen können. Dazu zählen v. a. das Ausmaß einer Resektion von Lungengewebe, kompensatorisches Lungenwachstum, Lungenhypoplasie und intensivmedizinische Maßnahmen wie maschinelle Beatmung. Durch hoch entwickelte chirurgische Techniken und eine verbesserte perioperative Intensivpflege können in zunehmendem Maß auch Patienten mit ausgeprägteren Defekten überleben, wenn auch um den Preis einer höheren Langzeitmorbidität.

Abstract

This article provides a brief review of the most important lower respiratory tract malformations, with particular focus on those factors that may have some impact on the long-term respiratory outcome of specific lesions. These factors include the amount of lung tissue resected, compensatory lung growth, lung hypoplasia, intensive care, and mechanical ventilation. With more sophisticated surgical techniques and constantly improving perioperative intensive care, patients with more severe defects will increasingly tend to survive in the future, though at the price of more severe long-term morbidity.

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  1. Klinische Abteilung für Pulmonologie und Allergologie, Universitätsklinik für Kinder- und Jugendheilkunde, Auenbruggerplatz 30, 8036 , Graz, Österreich

    G. H. Thalhammer, E. Eber & M. S. Zach

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  1. G. H. Thalhammer
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  2. E. Eber
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  3. M. S. Zach
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Correspondence to G. H. Thalhammer.

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Thalhammer, G.H., Eber, E. & Zach, M.S. Angeborene Fehlbildungen des unteren Respirationstraktes. Pneumologe 3, 372–380 (2006). https://doi.org/10.1007/s10405-006-0109-9

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