Persistent truncus arteriosus with absent semilunar valve in first trimester

  • Shui-hua YangEmail author
  • Xue-qin Li
  • Zuo-jian Yang
  • Xiao-xian Tian
  • Hong-wei Wei
Case Report


Persistent truncus arteriosus (PTA) is a relatively uncommon congenital heart disease, accounting for approximately 0.7–1.4% of all congenital cardiac abnormalities worldwide. PTA is usually accompanied by a single semilunar valve, with leaflets ranging from one to six in number. However, absent semilunar valve (ASV) is rarely seen in PTA. Here, we report a case of prenatally diagnosed PTA accompanied by ASV (PTA-ASV) confirmed by postmortem autopsy.


Persistent truncus arteriosus Absent semilunar valve Fetal echocardiography 



This work was supported by a grant from Guangxi Autonomous Region Construction Project of Clinical Research Center for Fetus Disease (No. AD17129016).

Compliance with ethical standards

Conflict of interest

There are no financial or other relations that could lead to a conflict of interest.


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Copyright information

© The Japan Society of Ultrasonics in Medicine 2019

Authors and Affiliations

  • Shui-hua Yang
    • 1
    Email author
  • Xue-qin Li
    • 1
  • Zuo-jian Yang
    • 1
  • Xiao-xian Tian
    • 1
  • Hong-wei Wei
    • 2
  1. 1.Department of UltrasoundThe Maternal and Child Health Hospital of Guangxi Zhuang Autonomous RegionNanningChina
  2. 2.Department of ObstetricsThe Maternal and Child Health Hospital of Guangxi Zhuang Autonomous RegionNanningChina

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