Abstract
The patient was a 26-year-old man who had undergone patch closure of a ventricular septal defect at 2 years of age. After this surgery, his condition was satisfactory until he visited our hospital for treatment of paroxysmal supraventricular tachycardia in November 2000. Echocardiography revealed moderate to severe aortic valve regurgitation and dilatation of the left ventricle and ascending aorta. These echocardiographic abnormalities were attributed to a bicuspid aortic valve. Coronary angiography suggested the presence of a single coronary artery originating from the left Valsalva sinus. We performed Bentall’s operation in January 2003. The intraoperative findings revealed that the aortic valve consisted of an extensively calcified single cusp, and there was a single coronary artery originating from the left Valsalva sinus. Because adult patients with a unicuspid aortic valve are rare, and no cases of unicuspid aortic valve associated with a single coronary artery have been reported, we herein report this case with a review of the literature.
Similar content being viewed by others
References
FF William (1992) Congenital heart disease in infancy and childhood Heart disease: a textbook of cardiovascular medicine Braunwald Philadelphia 922–9
JK Perloff (1978) The clinical recognition of congenital heart disease Saunders Philadelphia 81–113
BN Datta SD Deodhar PL Wahi (1976) ArticleTitleUnicuspid aortic valve in adults: report of two cases Indian Heart J 28 174–6 Occurrence Handle1:STN:280:CSiD1M3nvVM%3D Occurrence Handle1010537
JH Moller A Nakib RS Eliot et al. (1966) ArticleTitleSymptomatic congenital aortic stenosis in the first year of life J Pediatr 69 728–34 Occurrence Handle1:STN:280:CCiD2M3nslM%3D Occurrence Handle5928004
MW Falcone CR William GM Andrew et al. (1971) ArticleTitleCongenital aortic stenosis resulting from a unicommissural valve: clinical and anatomic features in twenty-one adult patients Circulation 44 272–80 Occurrence Handle1:STN:280:CS6B283mtV0%3D Occurrence Handle5562562
K Takenaka (1996) Aortic valve stenosis M Matsuzaki A Kitabatake (Eds) Heart disease practice 9: echocardiogram – determining therapy from Doppler record Bunkodo Press Tokyo 116–25
CS Passik DM Ackermann JR Pluth et al. (1987) ArticleTitleTemporal changes in the causes of aortic stenosis: a surgical pathologic study of 646 cases Mayo Clin Proc 62 119–23 Occurrence Handle1:STN:280:BiiC3MvhslE%3D Occurrence Handle3807436
MD Peterson RM Roach JE Edward et al. (1985) ArticleTitleType of aortic stenosis in surgically removed valves Arch Pathol Lab Med 109 829–32 Occurrence Handle1:STN:280:BiqB2sfmtFI%3D Occurrence Handle3839655
GM Novaro M Mishra BP Griffin (2003) ArticleTitleIncidence and echocardiographic features of congenital unicuspid aortic valve in an adult population J Heart Valve Dis 12 674–8 Occurrence Handle14658804
CS Roberts WC Robert (1991) ArticleTitleDissection of the aorta associated with congenital malformation of the aortic valve J Am Coll Cardiol 17 712–6 Occurrence Handle1:STN:280:By6C3s7ptV0%3D Occurrence Handle1993792
PWM Fedak S Verma TE David et al. (2002) ArticleTitleClinical and pathophysiological implication of a bicuspid aortic valve Circulation 106 900–4 Occurrence Handle10.1161/01.CIR.0000027905.26586.E8 Occurrence Handle12186790
JC Smith (1950) ArticleTitleReview of single coronary artery with report of 2 cases Circulation 1 1168–75 Occurrence Handle1:STN:280:Cy%2BD387jslU%3D Occurrence Handle15411739
H Takakura T Sasaki K Hashimoto et al. (2001) ArticleTitleA case of quadricuspid aortic valve associated with single coronary artery J Jpn Soc Cardiovasc Surg 30 26–8
BA Murphy L Groban ND Kon (2003) ArticleTitleDiagnosis of a unicuspid aortic valve using transesophageal echocardiography J Cardiothorac Vasc Anesth 17 82–3 Occurrence Handle10.1053/jcan.2003.15 Occurrence Handle12635067
Author information
Authors and Affiliations
Corresponding author
Additional information
This paper was presented at the 19th meeting of the Chubu Chapter of the Japan Society of Ultrasonics in Medicine.
About this article
Cite this article
Ishigami, H., Iwase, M., Hyoudo, K. et al. A case of unicuspid aortic valve associated with a single coronary artery and ventricular septal defect. J Med Ultrasonics 32, 65–70 (2005). https://doi.org/10.1007/s10396-005-0037-z
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/s10396-005-0037-z