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Das retrocavale extraadrenale Phäochromozytom als Zufallsbefund

An incidental finding of retrocaval extraadrenal pheochromocytoma

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Zusammenfassung

Im Rahmen der Abklärung eines 71- jährigen Patientens mit therapierefraktärer Hypertonie auf sekundäre Formen wurde eine extraadrenale Raumforderung gefunden. Nach weiterführender Bildgebung und biochemischer Abklärung wurde ein extraadrenales Phäochromozytom diagnostiziert, welches nach Alpha-Rezeptorblockade über einen posterioren Zugang laparoskopisch entfernt werden konnte. Das Phäochromozytom ist mit einer Inzidenz von 1–2 von 100.000 ein seltener katecholamin-produzierender Tumor. In etwa 1–25 % ist er extraadrenal lokalisiert. Zur Diagnosesicherung sollten die Hormonaktivität mittels Katecholaminbestimmung im Harn bzw. Plasma sowie eine Bildgebung erfolgen. Nach Blockade mit einem Alpha-Blocker stellt die komplette chirurgische Resektion die Therapie der Wahl dar.

Abstract

As part of diagnostic work-up of a 71-year-old patient with resistant hypertension, a extraadrenal mass was found. After further imaging and biochemical evaluation an extraadrenal pheochromocytoma was diagnosed and after alpha-receptor blockade was removed via posterior approach laparoscopically in the course. The pheochromocytoma is a rare catecholamine-producing tumor with an incidence of 1–2 per 100 000. In about 1–25 % it is located extraadrenal. Establishing the diagnosis is dependent on the demonstration of significant catecholamine excess. Afterwards imaging with CT or MRI should be performed. After administration of alpha-blockers, the complete surgical resection is the treatment of choice.

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Authors and Affiliations

  1. University of Salzburg, Müllner Hauptstraße 48, 5020, Salzburg, Österreich

    Katharina Maria Bretterbauer MD,  Daniela Colleselli MD,  Ahmed Magdy MD,  Günter Janetschek MD &  Michael Mitterberger MD

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  1. Katharina Maria Bretterbauer MD
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  2. Daniela Colleselli MD
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  3. Ahmed Magdy MD
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  4. Günter Janetschek MD
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  5. Michael Mitterberger MD
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Correspondence to Katharina Maria Bretterbauer MD.

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Bretterbauer, K.M., Colleselli, D., Magdy, A. et al. Das retrocavale extraadrenale Phäochromozytom als Zufallsbefund. Wien Med Wochenschr 165, 406–409 (2015). https://doi.org/10.1007/s10354-015-0374-5

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  • DOI: https://doi.org/10.1007/s10354-015-0374-5

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