European Surgery

, Volume 50, Issue 2, pp 68–72 | Cite as

A gastrointestinal stromal tumour mimicking solid pseudopapillary neoplasia of the pancreas—a case report

  • C. Müller
  • A. Beer
  • F. Wrba
  • T. Brodowicz
  • N. Bastati
  • A. Ba-Ssalamah
  • M. Schindl
case report



Diagnosis of large, heterogenous lesions of the pancreas with solid and cystic components is often challenging. The spectrum of differential diagnoses is broad, and clinical as well as radiological findings may be similar.


Detailed analysis of a clinical case and review of literature


We present the case of a 28-year-old woman with a large, heterogenous tumour of the pancreatic head that was incidentally found in routine ultrasound during pregnancy. The presence of a solid pseudopapillary neoplasm (SPN) was suspected because of typical clinical and radiological characteristics. The patient underwent partial pancreatoduodenectomy and surprisingly, histological work-up confirmed a pancreatic extra-gastrointestinal stromal tumour (EGIST).


As clinical and radiological findings may be misleading in a large, heterogenous tumour of the pancreas, a biopsy with histological proof of diagnosis is recommended, especially in situations where a neoadjuvant treatment may be considered.


Pancreatic disease Pancreatic neoplasm Surgical oncology Malignant mesenchymal tumour Diagnostic imaging 


Conflict of interest

C. Müller, A. Beer, F. Wrba, T. Brodowicz, N. Bastati, A. Ba-Ssalamah and M. Schindl declare that they have no competing interests.


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Copyright information

© Springer-Verlag GmbH Austria, part of Springer Nature 2018

Authors and Affiliations

  • C. Müller
    • 1
  • A. Beer
    • 2
  • F. Wrba
    • 2
  • T. Brodowicz
    • 3
  • N. Bastati
    • 4
  • A. Ba-Ssalamah
    • 4
  • M. Schindl
    • 1
  1. 1.Department of Surgery, Pancreatic Cancer Unit (PCU), Comprehensive Cancer Center ViennaMedical University of Vienna, General HospitalViennaAustria
  2. 2.Department of PathologyMedical University of Vienna, General HospitalViennaAustria
  3. 3.Division of Oncology, Department of Internal Medicine I, Comprehensive Cancer Center Vienna, Musculoskeletal Tumor UnitMedical University of Vienna, General HospitalViennaAustria
  4. 4.Department of Biomedical Imaging and Image-guided TherapyMedical University of Vienna, General HospitalViennaAustria

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