Skip to main content
SpringerLink
Log in

Hemisphärotomie bei einer 17-jährigen Patientin mit Sturge-Weber-Syndrom

Indikation und Follow-Up

Hemispherotomy in a 17-year-old patient with Sturge-Weber syndrome

Indication and follow-up

  • Der epilepsiechirurgische Fall
  • Published:
Zeitschrift für Epileptologie Aims and scope Submit manuscript

Zusammenfassung

Hemisphärotomien werden überwiegend im Kindesalter durchgeführt. Meist sind vorbestehende neurologische Defizite (homonyme Hemianopsie, Hemiparese) Vorraussetzung. Wir berichten von einer 17-jährigen Patientin mit medikamentenrefraktärer Epilepsie bei Sturge-Weber-Syndrom, die trotz fehlender Hemiparese und zusätzlicher idiopathisch generalisierter Epilepsie mit einer modifizierten Hemisphärotomie behandelt wurde. Postoperativ (11 Monate) war die Patientin anfallsfrei und gab trotz postoperativer spastischer Parese des linken Fußes eine deutliche Verbesserung der Alltagsfunktionalität und Lebensqualität an.

Abstract

Hemispherotomy is predominantly carried out in childhood. It can generally be assumed that preoperative neurological deficits (homonymous hemianopsia, hemiparesis) are present. We report on a 17-year-old patient with refractory epilepsy with Sturge-Weber syndrome who was treated with a modified hemispherotomy despite absence of hemiparesis and additional idiopathic generalized epilepsy. Postoperatively (11 months) the patient was seizure-free and, despite postoperative spastic paresis of the left foot, reported clearly improved everyday functioning and quality of life.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Abb. 1
Abb. 2
Abb. 3
Abb. 4
Abb. 5
Abb. 6

Literatur

  1. Basheer SN, Connolly MB, Lautzenhiser A et al (2007) Hemispheric surgery in children with refractory epilepsy: seizure outcome, complications, and adaptive function. Epilepsia 48:133–140

    Article  PubMed  Google Scholar 

  2. Bourgeois M, Crimmins DW, Santos de Oliveira R et al (2007) Surgical treatment of epilepsy in Sturge-Weber syndrome in children. J Neurosurg 106:20–28

    PubMed  Google Scholar 

  3. Devlin AM, Cross JH, Harkness W et al (2003) Clinical outcomes of hemispherectomy for epilepsy in childhood and adolescence. Brain 126:556–566

    Article  CAS  PubMed  Google Scholar 

  4. Di Rocco C, Tamburrini G (2006) Sturge-Weber syndrome. Childs Nerv Syst 22:909–921

    Article  Google Scholar 

  5. Kossoff EH, Buck C, Freeman JM (2002) Outcomes of 32 hemispherectomies for Sturge-Weber syndrome worldwide. Neurology 59:1735–1738

    PubMed  Google Scholar 

  6. Kossoff EH, Vining EPG, Pillas DJ et al (2003) Hemispherectomy for intractable unihemispheric epilepsy etiology vs outcome. Neurology 61:887–890

    CAS  PubMed  Google Scholar 

  7. Lüders H, Acharya J, Baumgartner C et al (1998) Semiological seizure classification. Epilepsia 39:1006–1013

    Article  PubMed  Google Scholar 

  8. Schramm J, Kral T, Clusmann H (2001) Transsylvian keyhole functional hemispherectomy. Neurosurgery 49:891–900

    Article  CAS  PubMed  Google Scholar 

  9. Steinhoff BJ, Staack AM, Bilic S et al (2009) Functional hemispherectomy in adults with intractable epilepsy syndromes: a report of 4 cases. Epileptic Disorder 11:251–257

    Google Scholar 

  10. Tuxhorn I, Holthausen H, Kotagal P, Pannek H (2008) In: Lüders HO (Hrsg) Textbook of epilepsy surgery. Informa, London, S 1249–1253

Download references

Interessenkonflikt

Der korrespondierende Autor gibt an, dass kein Interessenkonflikt besteht.

Author information

Authors and Affiliations

  1. Epilepsiezentrum Marburg, Klinik für Neurologie, Universitätsklinikum Gießen und Marburg GmbH, Philipps-Universität Marburg, Rudolf-Bultmann-Str. 8, 35309, Marburg, Deutschland

    A. Hermsen Dipl.-Psych., P.S. Reif, A. Haag, S. Bauer, H.M. Hamer & F. Rosenow

  2. Klinik für Neurochirurgie, Universitätsklinikum Bonn, Bonn, Deutschland

    J. Schramm

Authors
  1. A. Hermsen Dipl.-Psych.
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. P.S. Reif
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. A. Haag
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. S. Bauer
    View author publications

    You can also search for this author in PubMed Google Scholar

  5. H.M. Hamer
    View author publications

    You can also search for this author in PubMed Google Scholar

  6. J. Schramm
    View author publications

    You can also search for this author in PubMed Google Scholar

  7. F. Rosenow
    View author publications

    You can also search for this author in PubMed Google Scholar

Rights and permissions

Reprints and permissions

About this article

Cite this article

Hermsen, A., Reif, P., Haag, A. et al. Hemisphärotomie bei einer 17-jährigen Patientin mit Sturge-Weber-Syndrom. Z. Epileptol. 23, 259–263 (2010). https://doi.org/10.1007/s10309-010-0140-z

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s10309-010-0140-z

Schlüsselwörter

Keywords

Search

Navigation