Résumé
Les tumeurs rares du testicule et de ses annexes ont une incidence annuelle inférieure à 0,1 pour 100 000 hommes en France. Leur diversité est soulignée par la classification OMS de 2004, qui permet de distinguer plusieurs groupes en fonction de leur origine anatomique et de leur aspect histologique. Il en résulte une importante hétérogénéité pronostique et thérapeutique. La base d’une prise en charge optimale repose sur un œil d’expert anatomopathologique. La prise en charge thérapeutique qui en découle s’adapte à ce diagnostic. Avant tout chirurgicale, elle nécessite une stratégie pluridisciplinaire pour les tumeurs les plus agressives.
Abstract
Rare tumors of the testis and its annexes have an annual incidence of less than 0.1 per 100,000 men in France. Their diversity is emphasized by the WHO classification of 2004, which distinguishes several groups according to their anatomical origin and histology. It follows an important prognostic and therapeutic heterogeneity. Their optimal management is primarily based on pathological expertise. Surgery is the mainstay of treatment. A multi-disciplinary strategy is required for the most aggressive tumors.
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Compérat, E., Culine, S. Tumeurs rares du testicule et de ses annexes de l’adulte. Oncologie 16, 166–173 (2014). https://doi.org/10.1007/s10269-014-2382-2
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DOI: https://doi.org/10.1007/s10269-014-2382-2
Mots clés
- Cancer du testicule
- Tumeur rare
- Tumeur à cellules de Leydig
- Tumeur à cellules de Sertoli
- Lymphome primitif du testicule
- Tumeur adénomatoïde
- Cystadénome papillaire de l’épididyme
- Tumeurs primitives du cordon