Abstract
Among many other alterations of the skeletal structure, achondroplasia often presents alterations at the spinal level, which are represented by hyperkyphosis, especially at the thorax-lumbar level, with cuneiform deformation of the vertebral bodies, lumbar hyperlordosis caused by the position of the horizontal sacrum and stenosis of the vertebral canal, owing to the pedicles recesses. The treatment can be orthopaedic, by means of corsets or gymnastic, but in many cases, especially in the presence of neurologic injuries, a surgical care may be necessary, with wide decompressive laminectomies, associated with arthrodesis.
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Viganò, P., Misaggi, B. La terapia del paziente acondroplastico. Trattamento delle alterazioni del rachide. Arch Ortop Reumatol 120, 6–7 (2009). https://doi.org/10.1007/s10261-009-0031-x
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DOI: https://doi.org/10.1007/s10261-009-0031-x