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Hodgkin lymphoma as a complication of primary Sjögren’s syndrome

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Modern Rheumatology

Abstract

Sjögren’s syndrome (SS) is a chronic autoimmune disease that is characterized by lymphocytic infiltration of the exocrine glands, mainly the salivary and lachrymal glands, usually manifesting with xerostomia and xerophthalmia. Around 50% of patients with primary SS develop systemic complications, lymphoma being the most feared of these. The majority of these neoplasias originate from B cells and are of the non-Hodgkin type. We describe here a rare case of SS in which the patient developed a Hodgkin lymphoma. We also review the literature on this subject.

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Acknowledgments

MS is currently receiving a scholarship from Conselho Nacional de Desenvolvimento Científico e Tecnológico (CNPq). The authors acknowledge the technical assistance of Dr. Silene Barreto and Dr. Eduardo José Bittencourt (pathologists).

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Authors and Affiliations

  1. Rheumatology Service, Hospital Santa Izabel (HSI), Salvador, Bahia, Brazil

    Isabella Lima & Mittermayer Barreto Santiago

  2. Escola Bahiana de Medicina e Saúde Pública (EBMSP), Salvador, Bahia, Brazil

    Ana Suellen B. Carneiro, Caroline Alencar Amorim & Mittermayer Barreto Santiago

  3. Praça Conselheiro Almeida Couto, 500, Nazaré, Salvador, Bahia, CEP 40000-000, Brazil

    Mittermayer Barreto Santiago

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  1. Isabella Lima
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  2. Ana Suellen B. Carneiro
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  3. Caroline Alencar Amorim
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  4. Mittermayer Barreto Santiago
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Correspondence to Mittermayer Barreto Santiago.

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Lima, I., Carneiro, A.S.B., Amorim, C.A. et al. Hodgkin lymphoma as a complication of primary Sjögren’s syndrome. Mod Rheumatol 18, 200–202 (2008). https://doi.org/10.1007/s10165-008-0030-7

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  • DOI: https://doi.org/10.1007/s10165-008-0030-7

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