Neurological Sciences

, Volume 39, Issue 8, pp 1497–1499 | Cite as

Head tremor as a warning symptom of rapidly progressive syringomyelia: a case report

  • S. Mazzucchi
  • E. Unti
  • D. Frosini
  • F. Baldacci
  • R. Ceravolo
Letter to the Editor

The term syringomyelia indicates different types of spinal cord defects frequently associated to Arnold-Chiari I malformation (CM1). Natural history of the disease is unpredictable with a wide clinical spectrum, ranging from complete absence of neurological symptoms to a progressively disabling syndrome. Spontaneous radiological remission has been observed.

In a minority of cases, syringomyelia can present with involuntary movements. In the largest case series in literature [ 1], with a 15-year follow-up period, the presence of movement disorders was reported in 22 out of 100 patients with a newly diagnosed syringomyelia. Symptoms were mainly represented by spinal myoclonus, action hand tremor (usually lateralized), torticollis, blepharospasm, and abnormal head and arm postures. Further case reports described the presence of cervical dystonia or dystonia-athetosis of the hand or of the neck in patients with syringomielia [ 2, 3] (Table 1). The exact mechanism underlining this...


Compliance with ethical standards

The present research involved human participants and not animals; informed consent was obtained, and all procedures performed were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Conflict of interest

The authors declare that they have no conflict of interest.


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Copyright information

© Springer-Verlag Italia S.r.l., part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Clinical and Experimental MedicineUniversity of PisaPisaItaly
  2. 2.U.O. NeurologiaNuovo Ospedale ApuanoMassaItaly

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