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Rare combo: moyamoya and lupus in men

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Abstract

Moyamoya syndrome (MMS) is a rare, chronic, progressive cerebrovascular disorder characterized by stenosis at the apices of the intracranial internal carotid arteries, including the proximal anterior cerebral arteries and middle cerebral arteries. Cerebral angiography images are used for detection through measurement. Systemic lupus erythematosus (SLE) is an autoimmune disease that can cause multisystemic involvement. The coexistence of SLE and MMS has been rarely reported in the literature. A 46-year-old male patient with malar rash, Raynaud phenomenon presented to the hospital with a complaint of weakness in the left lower extremity, which began 3 days before the date of the visit. In the diffusion magnetic resonance imaging, multiple diffusion restrictions were observed in the right frontal region. The patient underwent MR angiography, revealing stenosis in the terminal and supraclinoid segments of the right internal carotid artery, which made us consider moyamoya disease. This patient, with a malar rash and Raynaud’s, a positive antibody profile, was diagnosed as a male with SLE accompanied by MMS.

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Authors and Affiliations

  1. Department of Rheumatology, Tekirdag Namik Kemal University, Tekirdag, Turkey

    Dilara Bulut Gökten & Rıdvan Mercan

  2. Department of Neurosurgery, Tekirdag City Hospital, Tekirdag, Turkey

    Murat Gökten

  3. Department of Neurology, Tekirdag Namik Kemal University, Tekirdag, Turkey

    Çiğdem Deniz

Authors
  1. Dilara Bulut Gökten
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  2. Murat Gökten
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  3. Çiğdem Deniz
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  4. Rıdvan Mercan
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Contributions

Dilara Bulut Gökten, data gathering, processing, writing, idea; Murat Gökten, data gathering and processing; Çiğdem Deniz, data gathering; Rıdvan Mercan, supervision, data gathering, idea.

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Correspondence to Dilara Bulut Gökten.

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Gökten, D.B., Gökten, M., Deniz, Ç. et al. Rare combo: moyamoya and lupus in men. Clin Rheumatol (2024). https://doi.org/10.1007/s10067-024-06960-1

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  • DOI: https://doi.org/10.1007/s10067-024-06960-1

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