Clinical Rheumatology

, Volume 37, Issue 5, pp 1153–1159 | Cite as

Infrequent organ involvement of IgG4-related diseases: a literature review

  • Jie Chang
  • Wen Zhang
Review Article


IgG4-related disease (IgG4-RD) is a chronic and systemic disease that can involve multiple organs. The most commonly involved organs include the salivary glands, orbital adnexal structures, paranasal sinus, thyroid, lungs, breasts, aorta, pancreas, biliary ducts, kidneys, retroperitoneum, lymph nodes, prostate, pituitary, and endocranium. Due to increased disease research, several new site-specific nuances of IgG4-RD have been described. The authors have reviewed the recent literature and briefly summarize the infrequent organ involvement of IgG4-RD.


IgG4-related disease Infrequent organ involvement Literature review Systemic disease 


Compliance with ethical standards




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© International League of Associations for Rheumatology (ILAR) 2018

Authors and Affiliations

  1. 1.Department of Rheumatology, The Fourth Affiliated HospitalZhejiang University School of MedicineZhejiang provinceChina
  2. 2.Department of Rheumatology, Peking Union Medical College HospitalChinese Academy of Medical Science and Peking Union Medical CollegeBeijingChina

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