Abstract
Sjogren’s syndrome (SS), either primary or secondary, is rarely accompanied by CNS complications. We report the exceptional case of a patient with secondary SS, who presented orofacial dystonia as a consequence of her disease. Initial treatment with clonazepam and levetiracetam was unsuccessful. However, dystonia was dramatically improved by a treatment with corticosteroids. This case demonstrates that corticosteroids can be efficacious in the treatment of dystonia related to SS.
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Papageorgiou, S.G., Kontaxis, T., Bonakis, A. et al. Orofacial dystonia related to Sjogren’s syndrome. Clin Rheumatol 26, 1779–1781 (2007). https://doi.org/10.1007/s10067-006-0519-4
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DOI: https://doi.org/10.1007/s10067-006-0519-4