Abstract
Congenital heart block (CHB) is the main complication of neonatal lupus (NL) and is strongly associated with the presence of anti-SSA/Ro and anti-SSB/La antibodies. The recurrence of CHB in subsequent pregnancies in mothers with these antibodies is uncommon, occurring in approximately 15% of cases. We describe here a case of recurrent CHB in a previously asymptomatic mother with Sjögren syndrome and discuss the current strategies for the prevention and treatment of CHB in NL.
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Escobar, M.C., Gómez-Puerta, J.A., Albert, D. et al. Recurrent congenital heart block in neonatal lupus. Clin Rheumatol 26, 1161–1163 (2007). https://doi.org/10.1007/s10067-006-0282-6
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DOI: https://doi.org/10.1007/s10067-006-0282-6