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Retroperitoneal fibrosis and c-ANCA positivity

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Abstract

Retroperitoneal fibrosis (RPF) is an uncommon collagen vascular disease characterized by a chronic nonspecific inflammation of the retroperitoneum, which can entrap and obstruct retroperitoneal structures. Although obscure, an autoimmune-mediated or vasculitic etiology has been hypothesized. In the current report, a case of RPF associated with the presence of antibodies against proteinase III, which responded effectively to immunosuppressive therapy, is presented.

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Authors and Affiliations

  1. Department of Pathophysiology, School of Medicine, National University of Athens, Athens, Greece

    Clio P. Mavragani & Michalis Voulgarelis

  2. Hospital for Special Surgery, 535 East 70th Street, New York, NY, 10021, USA

    Clio P. Mavragani

Authors
  1. Clio P. Mavragani
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  2. Michalis Voulgarelis
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Correspondence to Clio P. Mavragani.

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Mavragani, C.P., Voulgarelis, M. Retroperitoneal fibrosis and c-ANCA positivity. Clin Rheumatol 26, 115–116 (2007). https://doi.org/10.1007/s10067-005-0118-9

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  • DOI: https://doi.org/10.1007/s10067-005-0118-9

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