Abstract:
We here report on scleroderma renal crisis (SRC) appearing concurrently with isolated pulmonary hypertension (IPHT), that is, pulmonary hypertension without interstitial lung disease with fibrosis, in a patient with mixed connective tissue disease (MCTD) and in one with overlap syndrome or undifferentiated connective tissue disease (UCTD). To the best of our knowledge there are only five previous reports on SRC in MCTD and UCTD. The unexpected appearance of SRC in the setting of concomitant IPHT and limited or absent scleroderma skin changes is discussed.
Similar content being viewed by others
Author information
Authors and Affiliations
Additional information
Received: 26 January 2001 / Accepted: 13 July 2001
Rights and permissions
About this article
Cite this article
Andersen, G., Vasko, J. Scleroderma Renal Crisis and Concurrent Isolated Pulmonary Hypertension in Mixed Connective Tissue Disease and Overlap Syndrome: Report of Two Cases. Clin Rheumatol 21, 164–169 (2002). https://doi.org/10.1007/s10067-002-8276-5
Published:
Issue Date:
DOI: https://doi.org/10.1007/s10067-002-8276-5