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Primary Ocular Adnexal Lymphoma in Pediatric Patients: Report of Two Cases and Review of the Literature

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Pediatric and Developmental Pathology

Abstract

Primary ocular adnexal lymphoma (POAL) is a rare extranodal lymphoma. The mucosa-associated lymphoid tissue (MALT) subtype predominates and primarily occurs after the sixth decade of life. Most studies of ocular adnexal lymphoma are from the adult population. The data and experience in pediatric patients with POAL are limited to a few cases reported in the literature. Here we describe two pediatric cases of POAL and review the literature to further help characterize the clinical features and histopathologic appearance of this uncommon lymphoma.

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Fig. 1.

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Authors and Affiliations

  1. Department of Pathology, University of Colorado School of Medicine, 4200 East 9th Avenue B216, Denver, CO 80262, USA

    Xiayuan Liang

  2. Department of Pathology, The Children’s Hospital, 1056 East 19th Avenue B120, Denver, CO 80218, USA

    Xiayuan Liang

  3. Department of Pediatrics, University of Colorado School of Medicine, 4200 East 9th Avenue, Denver, CO 80262, USA

    Linda C. Stork & Edythe A. Albano

  4. Department of Hematology and Oncology, The Children’s Hospital, 1056 East 19th Avenue B115, Denver, CO 80218, USA

    Linda C. Stork & Edythe A. Albano

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  1. Xiayuan Liang
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  2. Linda C. Stork
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  3. Edythe A. Albano
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Correspondence to Xiayuan Liang.

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Liang, X., Stork, L. & Albano, E. Primary Ocular Adnexal Lymphoma in Pediatric Patients: Report of Two Cases and Review of the Literature . Pediatr. Dev. Pathol. 6, 458–463 (2003). https://doi.org/10.1007/s10024-003-1003-7

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  • DOI: https://doi.org/10.1007/s10024-003-1003-7

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