Oral and Maxillofacial Surgery

, Volume 22, Issue 2, pp 241–247 | Cite as

Intraosseous venous malformation of the zygomatico-orbital complex. Case report and literature review with focus on confusions in vascular lesion terms

  • Zoltán Fábián
  • György Szabó
  • Cecilia Petrovan
  • Karin Ursula Horváth
  • Botond Babicsák
  • Kálmán Hüttl
  • Zsolt Németh
  • Sándor Bogdán
Case Report


Intraosseous vascular malformations (VascM) of the facial skeleton are rare entities, raising difficulties even today in their treatment. We present a case for zygomatic intraosseous venous malformation of traumatic etiology with growth dynamics presentation and a multidisciplinary treatment approach, with intravascular embolization surgical ablation and primary reconstructruction using a titanium patient-specific implant (PSI), and a review of the literature for intraosseous vascular lesions of the facial skeleton focusing on the diagnostic syntagms used by the involved medical personnel, to shed light on the confusions over these terms.


Intraosseous venous malformation Vascular malformations Patient-specific implants Superselective embolisation 



We wish to thank to Sebastian Condrea, Mocanu Simona, Bögözi Bálint, and especially for János Kónya for his expertise and help in creating the PSI.

Author’s contributions

ZF: conceived the article, data analysis, writing of manuscript, PSI planning, surgery.

GYSZ: interdisciplinary coordination, writing of manuscript, critically revised the manuscript, surgery.

CP: manuscript review, patient investigations, follow-up.

BB: postoperative care, embolization, surgery, data acquisition.

KUH: ophthalmologic supervision-follow-up, data acquisition, drafting the manuscript.

KH: performed the embolization procedure, processing the images of the angiography, manuscript review.

ZN: critically revised the manuscript, approved the final manuscript.

SB: interdisciplinary coordination, performed the surgical procedure, data acquisition, and interpretation, drafting the manuscript, final approval of the manuscript.

All authors read and approved the final manuscript.

Compliance with ethical standards

This article does not contain any studies with human participants or animals performed by any of the authors. The treatment of the presented patient was not in any way influenced the due to this article.


The legal representative of the patient signed an explicit authorization form to publish the pictures without eye masking or with any other identifiable information. A copy of the authorization will be provided to the publisher upon request.

Competing interests

Zoltán Fábián declares that he has no conflict of interest.

György Szabó declares that he has no conflict of interest.

Cecilia Petrovan declares that he has no conflict of interest.

Karin Ursula Horváth declares that he has no conflict of interest.

Botond Babicsák declares that he has no conflict of interest.

Kálmán Hüttl declares that he has no conflict of interest.

Zsolt Németh declares that he has no conflict of interest.

Sándor Bogdán declares that he has no conflict of interest.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  • Zoltán Fábián
    • 1
  • György Szabó
    • 2
  • Cecilia Petrovan
    • 3
  • Karin Ursula Horváth
    • 4
  • Botond Babicsák
    • 2
  • Kálmán Hüttl
    • 5
  • Zsolt Németh
    • 2
  • Sándor Bogdán
    • 2
  1. 1.University of Medicine and PharmacyTârgu MureșRomania
  2. 2.Department of Oro-Maxillofacial Surgery and StomatologySemmelweis UniversityBudapestHungary
  3. 3.Department of Oral and Maxillofacial SurgeryCounty Clinical Emergency HospitalTârgu MureșRomania
  4. 4.Department of OphthalmologyMureș County Clinical HospitalTârgu MureșRomania
  5. 5.Heart and Vascular CenterSemmelweis UniversityBudapestHungary

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