Abstract
Introduction
Hemophilic pseudotumor is a rare complication occurring in patients with hemophilia, frequently seen in the femur, tibia, pelvic bones, iliac bones, or rarely in the maxillofacial region.
Case report
A 7-year-old male reported with a spontaneous extra-oral swelling that was managed with pre-operative transfusion of factor IX along with curettage of the lesion. Our report presents only the fourth case in literature wherein this tumor presented in a patient with hemophilia B.
Finding
Hemophilic pseudotumor is a rare entity in the maxillofacial region. High degree of suspicion is required for diagnosis, and close coordination between the medical and surgical teams aids in management.
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Chattopadhyay, P.K., Nagori, S.A., Menon, R.P. et al. Hemophilic pseudotumor of the mandible in a patient with hemophilia B. Oral Maxillofac Surg 21, 467–469 (2017). https://doi.org/10.1007/s10006-017-0647-9
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DOI: https://doi.org/10.1007/s10006-017-0647-9