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Formen der Vaskulitis

Types of vasculitis

Zusammenfassung

Die Vaskulitiden sind (zumeist seltene) entzündliche Gefäßerkrankungen mit sehr heterogenem klinischem Erscheinungsbild. Sie können akut auftreten und lebensbedrohlich sein und erfordern häufig eine interdisziplinäre Zusammenarbeit bei Diagnostik und Therapie. Dieser Artikel soll einen Überblick über die verschiedenen Formen v. a. der systemischen Vaskulitiden und ihrer Klassifikation anhand der Nomenklatur der Vaskulitiden der internationalen Chapel-Hill-Konsensuskonferenz (CHCC) von 2012 geben. Dabei stehen klinische Erscheinungsformen und diagnostische Maßnahmen für die häufigsten Vaskulitiden großer, mittelgroßer und kleiner Gefäße im Mittelpunkt.

Abstract

Vasculitides are (mostly rare) inflammatory diseases of blood vessels with very heterogeneous clinical symptoms. They can manifest suddenly and be potentially life-threatening and frequently necessitate an interdisciplinary cooperation for diagnostics and treatment. This article reviews the various forms and in particular systemic vasculitides and the nomenclature according to the 2012 International Chapel Hill Consensus Conference (CHCC) classification. The review focuses on clinical manifestations and diagnostic procedures for the more frequent forms of large, medium and small vessel vasculitis.

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Correspondence to M. O. Becker.

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Interessenkonflikt

M. O. Becker, B. Maurer und O. Distler geben an, dass kein Interessenkonflikt besteht.

Dieser Beitrag beinhaltet keine von den Autoren durchgeführten Studien an Menschen oder Tieren.

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Becker, M.O., Maurer, B. & Distler, O. Formen der Vaskulitis. Gefässchirurgie 24, 104–113 (2019). https://doi.org/10.1007/s00772-018-0499-0

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  • DOI: https://doi.org/10.1007/s00772-018-0499-0

Schlüsselwörter

  • Systemische Vaskulitis
  • Klassifikation
  • Diagnostik
  • ANCA-assoziierte Vaskulitis
  • Arteriitis

Keywords

  • Systemic vasculitis
  • Classification
  • Diagnosis
  • ANCA-associated vasculitis
  • Arteritis