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Intimasarkom der Aorta abdominalis (epitheloides Angiosarkom) mit Tumorembolie der A. poplitea

Intimal sarcoma of the abdominal aorta (epithelioid angiosarcoma) with tumor embolism of the popliteal artery

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Zusammenfassung

Das Intimasarkom der Aorta abdominalis ist ein maligner Gefäßtumor, der eine periphere arterielle Verschlusskrankheit (pAVK) vortäuschen kann. Wir berichten über den Fall eines epitheloiden Angiosarkoms der Aorta abdominalis und A. iliaca communis mit Tumorembolie der A. poplitea und den Symptomen einer pAVK im Stadium IV. Aufgrund des ungewöhnlichen Angiographiebefundes wurde die Verdachtsdiagnose gestellt. Sowohl der aortoiliakale als auch der popliteale Abschnitt wurden deshalb primär reseziert. Die Diagnose wurde immunhistologisch in den Resektaten verifiziert. Es verbleiben Unklarheiten hinsichtlich des biologischen Verhaltens und der chirurgischen sowie adjuvanten Therapie dieses seltenen malignen Tumors.

Abstract

Intimal sarcoma of the abdominal aorta is a malignant vascular tumor simulating peripheral arterial disease. We report the case of an epithelioid angiosarcoma of the abdominal aorta and common iliac artery with tumor embolism of the popliteal artery. The unusual angiographic appearance suggested the tumor diagnosis. Primary resection of the involved aortoiliac segments and the left popliteal artery was therefore done. Immunohistological analysis of the resected specimens verified the diagnosis. Uncertainty persists regarding the biological behavior and operative as well as adjuvant therapy.

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Authors and Affiliations

  1. Klinik für Gefäßchirurgie, Klinikum Chemnitz, Bürgerstr. 2, 09113, Chemnitz, Deutschland

    A. Schröder & M. Koch

  2. Klinik für Innere Medizin I, Klinikum Chemnitz, Chemnitz, Deutschland

    J. Schweizer

  3. Institut für Diagnostische Radiologie, Klinikum Chemnitz, Chemnitz, Deutschland

    W. Volkmar

  4. Institut für Pathologie, Klinikum Chemnitz, Chemnitz, Deutschland

    J.O. Habeck

Authors
  1. A. Schröder
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  2. M. Koch
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  3. J. Schweizer
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  4. W. Volkmar
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  5. J.O. Habeck
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Correspondence to A. Schröder.

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Schröder, A., Koch, M., Schweizer, J. et al. Intimasarkom der Aorta abdominalis (epitheloides Angiosarkom) mit Tumorembolie der A. poplitea. Gefässchirurgie 13, 417–420 (2008). https://doi.org/10.1007/s00772-008-0609-5

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  • DOI: https://doi.org/10.1007/s00772-008-0609-5

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