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Optikushypoplasie

Optic nerve hypoplasia

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Zusammenfassung

Die richtige Interpretation und rechtzeitige Erhebung des ophthalmoskopischen Befundes einer „kleinen Papille“ liefert wichtige Hinweise auf die weitere Visusentwicklung bei Kindern und kann auf andere Anomalien des Zentralnervensystems aufmerksam machen. Bei der Opticushypoplasie (ONH) handelt es sich um eine der häufigsten Papillenanomalien. Ophthalmoskopisch erscheint hier der Sehnervenkopf deutlich kleiner.

Die Opticushypoplasie gehört zu den häufigsten Ursachen einer kongenitalen Sehbehinderung. Kinder mit Opticushypoplasie sollten auf andere systemische Erkrankungen und Missbildungen untersucht werden, sowie einer Sehfrühförderung zugeführt werden. Die frühe interdisziplinäre Zusammenarbeit zwischen Ophtalmologen und Pädiatern ist hier besonders herausfordernd und essentiell.

Summary

Correct interpretation of the ophthalmoscopic finding “small disc” gives an important hint of the visual development in children and is associated with other anomalies of the central nervous system and endocrine abnormalities. Hypoplasia of the optic nerve is one of the most common anomalies of the optic disc. In the ophthalmoscopic examination the optic nerve head appears small.

Hypoplasia of the optic nerve is one of the most common causes of severe visual impairment in children. Children with ONH should be screened for endocrine abnormalities as well as congenital anomalies of the central nervous system. ONH represents a demanding challenge for early interdisciplinary cooperation between pediatriacian and ophthalmologist.

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Authors and Affiliations

  1. Institut für Orthoptik – Sehschule, Konventhospital der Barmherzigen Brüder, Seilerstätte 2, 4021, Linz, Österreich

    Vassilis Kessaris FEBO

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  1. Vassilis Kessaris FEBO
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Correspondence to Vassilis Kessaris FEBO.

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Kessaris, V. Optikushypoplasie. Spektrum Augenheilkd. 26, 253–256 (2012). https://doi.org/10.1007/s00717-012-0127-4

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  • DOI: https://doi.org/10.1007/s00717-012-0127-4

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