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Primary ectopic orbital craniopharyngioma

  • Case Report - Brain Tumors
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Abstract

Craniopharyngiomas (CP) ectopic localizations off the midline outside the sellar-suprasellar region are very rare and most often associated to secondary tumor dissemination, being primary ectopic CPs extremely unusual. We herein report the first case of a primary ectopic craniopharyngioma within the orbit. A 15-year-old patient presented with progressive right ptosis, proptosis, and retro ocular pain. Magnetic resonance imaging (MRI) showed a predominantly cystic lesion, occupying the superolateral right corner of the orbit, outside the intraconal space with no evidence of intracranial involvement. An endoscopic transorbital eyelid approach was adopted. Pathology report disclosed a primary ectopic craniopharyngioma.

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Authors and Affiliations

  1. Department of Neurosciences and Reproductive and Dental Sciences, Division of Neurosurgery, Federico II University of Naples, Policlinico Federico II University Hospital, Via Sergio Pansini, 5, 80131, Napoli, Italy

    Francesca Vitulli, Elena D’Avella, Domenico Solari & Luigi Maria Cavallo

  2. Department of Advanced Biomedical Sciences, Pathology Unit, Federico II University of Naples, Naples, Italy

    Raduan Ahmed Franca

  3. Department of Neurosciences and Reproductive and Dental Sciences, Division of Maxillofacial Surgery Unit, Federico II University of Naples, Naples, Italy

    Antonio Romano & Paola Bonavolontà

Authors
  1. Francesca Vitulli
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  2. Elena D’Avella
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  3. Domenico Solari
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  4. Raduan Ahmed Franca
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  5. Antonio Romano
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  6. Paola Bonavolontà
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  7. Luigi Maria Cavallo
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Correspondence to Francesca Vitulli.

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This article is part of the Topical Collection on Brain Tumors

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Supplementary file1 Removal of a primary ectopic craniopharyngioma thought an endoscopic transorbital eyelid approach. (MP4 264424 KB)

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Vitulli, F., D’Avella, E., Solari, D. et al. Primary ectopic orbital craniopharyngioma. Acta Neurochir 164, 1979–1984 (2022). https://doi.org/10.1007/s00701-021-04969-y

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  • DOI: https://doi.org/10.1007/s00701-021-04969-y

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