Intrachiasmatic abscess caused by IgG4-related hypophysitis

  • Georgios F. Hadjigeorgiou
  • Eva Løbner Lund
  • Lars Poulsgaard
  • Ulla Feldt-Rasmussen
  • Åse Krogh Rasmussen
  • Marianne Wegener
  • Kåre Fugleholm
Case Report - Brain Tumors

Abstract

Introduction

Autoimmune hypophysitis is a rare disease of the pituitary, which may affect vision by inflammation and compression of the optic chiasm. However, intrachiasmatic abscess formation has not been previously reported.

Methods

In this study, we report a case of a 29-year-old female with bitemporal hemianopia due to a cystic intrasellar tumor. The patient underwent surgical decompression of the lesion, which was found to be an intrachiasmatic abscess.

Results

The histologic findings were consistent with IgG4 hypophysitis.

Conclusion

This rare clinical presentation suggests that in case of a disproportionate degree of visual impairment in relation to the size of the lesion, suspicion should lead to an intrachiasmatic lesion.

Keywords

Abscess Hypophysitis IgG4 Intrachiasmatic 

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Copyright information

© Springer-Verlag GmbH Austria 2017

Authors and Affiliations

  • Georgios F. Hadjigeorgiou
    • 1
  • Eva Løbner Lund
    • 2
  • Lars Poulsgaard
    • 3
  • Ulla Feldt-Rasmussen
    • 4
  • Åse Krogh Rasmussen
    • 4
  • Marianne Wegener
    • 5
  • Kåre Fugleholm
    • 3
  1. 1.Department of Neurosurgery, Academic Hospital Munich-BogenhausenTechnical University of MunichMunichGermany
  2. 2.Department of PathologyUniversity Hospital of CopenhagenCopenhagenDenmark
  3. 3.Department of NeurosurgeryUniversity Hospital of CopenhagenCopenhagenDenmark
  4. 4.Department of EndocrinologyUniversity Hospital of CopenhagenCopenhagenDenmark
  5. 5.Department of Neuro-opthalmologyUniversity Hospital of CopenhagenCopenhagenDenmark

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