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Acta Neurochirurgica

, Volume 152, Issue 9, pp 1619–1621 | Cite as

Meningioma-like lesions in Erdheim Chester disease

  • Rohana Naqi
  • Muhammad Azeemuddin
  • Romana Idrees
  • Mohammad WasayEmail author
Letter to the editor

Dear Sir,

We are reporting a woman with bilateral, multiple, extra-axial-enhancing lesions mimicking meningiomas. Histopathology of lesions revealed the diagnosis of Erdheim Chester disease (ECD). This report provides clinical and neuroimaging findings of this disease and clues for presurgical diagnosis of ECD.

Case report

A 55-year-old female patient, a hypertensive, was admitted with generalized tonic clonic seizures, fever, cough, and drowsiness. Her symptoms had started 1 month back. Detailed work-up was done, and she was diagnosed to have diabetes insipidus. Her laboratory investigations showed hypernatremia with serum sodium level of 170, WBC count was 21.2, ESR was 94, and C-reactive protein was 20.5. Her chest X-ray showed osteopenia of visualized bone with patchy bony density at lateral ends of both clavicles. Radionuclide skeletal scintigraphy revealed diffusely increased tracer uptake over appendicular skeleton and left hemipelvis, with evidence of bony expansion and photon...

Keywords

Meningioma Diabetes Insipidus Esomeprazole Desmopressin Histiocytosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Notes

Acknowledgement

Authors are grateful to Prof. Ather Enam FRCS, MD, PhD, Head of Neurosurgery at Aga Khan University for his contribution.

References

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Copyright information

© Springer-Verlag 2010

Authors and Affiliations

  • Rohana Naqi
    • 1
  • Muhammad Azeemuddin
    • 1
  • Romana Idrees
    • 2
  • Mohammad Wasay
    • 3
    Email author
  1. 1.Department of RadiologyAga Khan UniversityKarachiPakistan
  2. 2.Department of PathologyAga Khan UniversityKarachiPakistan
  3. 3.Department of Medicine/NeurologyThe Aga Khan UniversityKarachiPakistan

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