Skip to main content

Advertisement

SpringerLink
Log in

Sturge-Weber syndrome accompanied with multiple congenital intracranial lesions

  • Case Report
  • Published:
Acta Neurochirurgica Aims and scope Submit manuscript

Summary

Sturge-Weber syndrome is one of the neurocutaneous syndromes. It is a rare, nonfamiliar disease that is characterized by facial port-wine stain, leptomeningeal angiomatosis, choroidal angioma, buphthalmos, intracranial calcification, cerebral atrophy, mental retardation, glaucoma, seizures and hemiparesis. CT and MR are complementary in the evaluation of this disease. Epilepsy is an essential feature of Sturge-Weber syndrome and it has a major significance for prognosis and treatment. We report a 2-year-old boy with Sturge-Weber syndrome who had in addition an intracranial lipoma, a temporal arachnoid cyst and a porencephalic cyst. This combination of intracranial lesions with Sturge-Weber syndrome has not been previously reported.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

References

  • E Akpinar (2004) ArticleTitleThe tram-track sign: cortical calcifications Radiology 231 515–516 Occurrence Handle15128996 Occurrence Handle10.1148/radiol.2312020545

    Article  PubMed  Google Scholar 

  • A Arzimanoglou J Aicardi (1992) ArticleTitleThe epilepsy of Sturge-Weber syndrome: clinical features and treatment in 23 patients Acta Neurol Scand (Suppl) 140 18–22 Occurrence Handle1:STN:280:DyaK3s%2FntVymsg%3D%3D Occurrence Handle10.1111/j.1600-0404.1992.tb04465.x

    Article  CAS  Google Scholar 

  • A Arzimanoglou F Andermann J Aicardi C Sainte-Rose MA Beaulieu JG Villemure A Olivier Th Rasmussen (2000) ArticleTitleSturge-Weber syndrome. Indications and results of surgery in 20 patients Neurology 55 1472–1479 Occurrence Handle11094100 Occurrence Handle1:STN:280:DC%2BD3M%2FmvFKnsQ%3D%3D

    PubMed  CAS  Google Scholar 

  • ES Roach AR Riela HT Chugani (1994) ArticleTitleSturge-Weber syndrome. Recommendations for surgery J Child Neurol 9 190–192 Occurrence Handle8006373 Occurrence Handle1:STN:280:DyaK2c3nsFWjtw%3D%3D

    PubMed  CAS  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Department of Neurosurgery, Abant İzzet Baysal University, Bolu, Turkey

    R. Ergün & A. R. Gezici

  2. Department of Neurosurgery, Numune Hospital, Adana, Turkey

    A. İ. Ökten & Y. Gezercan

Authors
  1. R. Ergün
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. A. İ. Ökten
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. Y. Gezercan
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. A. R. Gezici
    View author publications

    You can also search for this author in PubMed Google Scholar

Rights and permissions

Reprints and permissions

About this article

Cite this article

Ergün, R., Ökten, A., Gezercan, Y. et al. Sturge-Weber syndrome accompanied with multiple congenital intracranial lesions. Acta Neurochir (Wien) 149, 829–830 (2007). https://doi.org/10.1007/s00701-007-1224-z

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s00701-007-1224-z

Search

Navigation