Skip to main content
Log in

Tumorectomy with right thoracotomy for synchronous left atrial myxomas from Carney complex: report of a case

  • Case Report
  • Published:
Surgery Today Aims and scope Submit manuscript


This report describes a case of synchronous left atrial myxomas from Carney complex resected through a right thoracotomy. The patient was a 30-year-old female that had previously been diagnosed with Carney complex following a genetic examination. Preoperative echocardiography showed a left atrial tumor, but intraoperative inspection revealed another tumor in the left atrium. Carney complex was first described in the 1980s and cardiac myxoma from Carney complex can occur in any cardiac chamber, presenting multiple times with postoperative recurrences, occurring at any age and without any predilection for gender, and is inherited in an autosomal-dominant manner. Treatment for cardiac myxoma from Carney complex is very important for patient mortality and morbidity and, despite the endocrine nature of the disorder, cardiologists and cardiac surgeons play an important role.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Fig. 1
Fig. 2
Fig. 3


  1. Stratakis CA, Kirschner LS, Carney JA. Clinical and molecular features of the Carney complex: diagnostic criteria and recommendations for patient evaluation. J Clin Endocrinol Metab. 2001;86:4041–6.

    Article  CAS  PubMed  Google Scholar 

  2. Shenoy BV, Carpenter PC, Carney JA. Bilateral primary pigmented nodular adrenocortical disease. Rare cause of the Cushing syndrome. Am J Surg Pathol. 1984;8:335–44.

    Article  CAS  PubMed  Google Scholar 

  3. Carney JA, Gordon H, Carpenter PC, Shenoy BV, Go VL. The complex of myxomas, spotty pigmentation, and endocrine overactivity. Medicine (Baltimore). 1985;64:270–83.

    Article  CAS  Google Scholar 

  4. Bain J. Carney’s Complex. Mayo Clin Proc. 1986;61:508.

    Article  CAS  PubMed  Google Scholar 

  5. Kirschner LS, Carney JA, Pack SD, Taymans SE, Giatzakis C, Cho YS, et al. Mutations of the gene encoding the protein kinase A type I-alpha regulatory subunit in patients with the Carney complex. Nat Genet. 2000;26(1):89–92.

    Article  CAS  PubMed  Google Scholar 

  6. Boikos SA, Stratakis CA. Carney complex: pathology and molecular genetics. Neuroendocrinology. 2006;83:189–99.

    Article  CAS  PubMed  Google Scholar 

  7. Greelish JP, Chatterjee S, Byrne JG. Recurrent atrial myxoma: resection for Carney complex through a minimally invasive approach. J Card Surg. 2010;25:519–21.

    Article  PubMed  Google Scholar 

  8. Shetty Roy AN, Radin M, Sarabi D, Shaoulian E. Familial recurrent atrial myxoma: Carney’s complex. Clin Cardiol. 2011;34:83–6.

    Article  PubMed  Google Scholar 

  9. McCarthy PM, Piehler JM, Schaff HV, Pluth JR, Orszulak TA, Vidaillet HJ Jr, et al. The significance of multiple, recurrent, and “complex” cardiac myxomas. J Thorac Cardiovasc Surg. 1986;91:389–96.

    CAS  PubMed  Google Scholar 

  10. Bireta C, Popov AF, Schotola H, Trethowan B, Friedrich M, El-Mehsen M, et al. Carney-Complex: multiple resections of recurrent cardiac myxoma. J Cardiothorac Surg. 2011;6:12.

    Article  PubMed Central  PubMed  Google Scholar 

Download references

Conflict of interest

Narihiro Ishida and the co-authors have no conflicts of interest to declare.

Author information

Authors and Affiliations


Corresponding author

Correspondence to Narihiro Ishida.

Rights and permissions

Reprints and permissions

About this article

Cite this article

Ishida, N., Shimabukuro, K., Matsuno, Y. et al. Tumorectomy with right thoracotomy for synchronous left atrial myxomas from Carney complex: report of a case. Surg Today 44, 185–187 (2014).

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: