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Fibular grafting in diaphyseal Gorham’s disease: report of two cases and review of literature

  • Sujit Kumar TripathyEmail author
  • Ramesh Kumar Sen
  • Amit Agarwal
Case Report

Abstract

Gorham’s disease of bone is a rare entity where the bone undergoes progressive osteolysis. Management of diaphyseal Gorham’s disease is a real challenge to manage as a large bony defect is created because of osteolysis. We report two such cases where we reconstructed the defect with fibular graft after a radiation dose of 30 Gy. The graft was well incorporated and radiological sign of union was noticed in proximal and distal metaphysis after a follow-up of 4 and 2 years. Fibular grafting can be a good method of reconstruction in diaphyseal Gorham’s disease of long bone, provided the diseased tissue has been excised adequately after local radiation therapy.

Keywords

Gorham’s disease Fibular grafting Progressive idiopathic osteolysis Diaphyseal Gorham’s disease 

Notes

Acknowledgment

No funds were received in support of this study.

Conflict of interest statement

No benefits in any form have been or will be received from a commercial party related directly or indirectly to the subject of this manuscript.

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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Sujit Kumar Tripathy
    • 1
    • 3
    Email author
  • Ramesh Kumar Sen
    • 1
    • 3
  • Amit Agarwal
    • 1
    • 2
    • 3
  1. 1.Department of OrthopaedicsPGIChandigarhIndia
  2. 2.Department of OrthopaedicsAIIMSNew DelhiIndia
  3. 3.Postgraduate Institute of Medical Education and ResearchChandigarhIndia

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