Journal of Anesthesia

, Volume 30, Issue 6, pp 1087–1090 | Cite as

Biphasic cuirass ventilation for treatment of an air leak after pneumothorax in a patient with nemaline myopathy: a case report

  • Hitomi HinoEmail author
  • Yuka Suzuki
  • Eiichi Ishii
  • Mitsumasa Fukuda
Clinical Report


We describe an 11-year-old boy with nemaline myopathy who developed tension pneumothorax while undergoing noninvasive positive-pressure ventilation (NIPPV). The patient developed a persistent air leak after pleurodesis with minocycline hydrochloride and lowering of the NIPPV inspiratory pressure. He required additional respiratory support without the high airway pressures that may aggravate pneumothorax. We provided adequate respiratory support without increasing the positive airway pressure using biphasic cuirass ventilation (BCV), which moved the patient’s chest wall by negative pressure. The air leak was resolved without any additional treatment. We should provide BCV for patients in whom surgery may have a risk of both extubation failure and postoperative complications before deciding on surgery.


Pediatrics Neurology Ventilation Pneumothorax 



We thank Drs. Shungo Yukumi and Yasuaki Kashu for their assistance with the treatment of the patient.


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Copyright information

© Japanese Society of Anesthesiologists 2016

Authors and Affiliations

  • Hitomi Hino
    • 1
    Email author
  • Yuka Suzuki
    • 2
  • Eiichi Ishii
    • 1
  • Mitsumasa Fukuda
    • 1
  1. 1.Department of PediatricsEhime University Graduate School of MedicineToonJapan
  2. 2.Department of PediatricsMatsuyama Red Cross HospitalMatsuyamaJapan

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