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Anesthetic management of noncardiac surgery for patients with single ventricle physiology

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Abstract

Patients with congenital heart diseases are a growing population, and noncardiac surgeries will become an important health care issue. Patients with single ventricle physiology are a particularly challenging population who will undergo staged, palliative repair toward a final step of Fontan circulation. Although Fontan surgery creates a serial circulation in which the ventricle pumps blood to the systemic circuit, pulmonary blood flow occurs without a dedicated ventricle. Despite progress in outcomes, this abnormal circulation remains associated with various co-morbidities such as ventricular dysfunction, arrhythmias, protein losing enteropathy, and plastic bronchitis. Health care professionals must prepare for these patients to present to noncardiac surgery at any stage of intervention, possibly with complications. Given that staged, palliative repair has undergone multiple modifications, patients who present for surgery can vary in types and timing of the repair. Anesthesiologists who care for them must be familiar with perioperative issues to optimize outcomes, especially because congenital heart disease is a risk factor for increased mortality for noncardiac surgery.

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Acknowledgments

This is supported in part by Grant-in-Aid for Scientific Research© (nos. 20591844 and 18591726) (S.Uezono).

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Authors and Affiliations

  1. Department of Anesthesiology, Perioperative and Pain Medicine, Childrens Hospital Boston, 300 Longwood Avenue, Bader 3, Boston, MA, 02115, USA

    Koichi Yuki & Alfonso Casta

  2. Department of Anaesthesia, Harvard Medical School, Boston, MA, USA

    Koichi Yuki & Alfonso Casta

  3. Department of Anesthesiology, Jikei University, Tokyo, Japan

    Shoichi Uezono

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  1. Koichi Yuki
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Correspondence to Koichi Yuki.

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Yuki, K., Casta, A. & Uezono, S. Anesthetic management of noncardiac surgery for patients with single ventricle physiology. J Anesth 25, 247–256 (2011). https://doi.org/10.1007/s00540-010-1081-4

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