Abstract
Congenital erythropoietic porphyria is a rare error of heme metabolism. Derangement of heme metabolism leads to disfiguration, phototoxicity, and the precipitation of porphyric crises. This case report discusses the myriad perioperative considerations in a patient with congenital erythropoietic porphyria.
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Kumar, M., Bose, S., Darlong, V. et al. Congenital erythropoietic porphyria: anesthetic implications. J Anesth 23, 569–571 (2009). https://doi.org/10.1007/s00540-009-0784-x
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DOI: https://doi.org/10.1007/s00540-009-0784-x