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Anesthetic management of two cases of Beckwith-Wiedemann syndrome

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Abstract

Two cases of children with Beckwith-Wiedemann syndrome are presented. This syndrome consists of various abnormalities, including macroglossia, visceromegaly, omphalocele, and gigantism. These abnormalities frequently require operative correction during the neonatal period. We anesthesiologists should make plans for difficult airway managements in patients with this syndrome. Our two patients also showed larger sized tracheas than those estimated by their age and height. A cuffed tube, though still controversial, has recently been used in children. We recommend using a cuffed tube in patients with this syndrome, because the appropriate tracheal size may not be predictable, tracheal intubation might be difficult, and risks incurred during changing of a tracheal tube should be avoided.

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Authors and Affiliations

  1. Department of Anesthesia, Takikawa Municipal Hospital, 2-34-2 Omachi, Takikawa, 073-0022, Japan

    Yoshinobu Kimura

  2. Department of Anesthesia, Nikko Memorial Hospital, Muroran, Japan

    Yasuhiro Kamada

  3. Department of Anesthesiology, Sapporo Medical University, Sapporo, Japan

    Saori Kimura

Authors
  1. Yoshinobu Kimura
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  2. Yasuhiro Kamada
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  3. Saori Kimura
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Kimura, Y., Kamada, Y. & Kimura, S. Anesthetic management of two cases of Beckwith-Wiedemann syndrome. J Anesth 22, 93–95 (2008). https://doi.org/10.1007/s00540-007-0571-5

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  • DOI: https://doi.org/10.1007/s00540-007-0571-5

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