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Life-threatening acute pneumonitis in mixed connective tissue disease: a case report and literature review

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Summary

Mixed connective tissue disease (MCTD) is a rare connective tissue disease frequently involving the lungs. The main characteristic is a systemic sclerosis-like picture of slowly progressing interstitial lung disease consistent with lung fibrosis, while pulmonary arterial hypertension is rare. Herein, we present a case of a newly diagnosed MCTD patient developing life-threatening acute pneumonitis similar to lupus pneumonitis. Previous literature on this exceptionally rare complication of MCTD is reviewed and differential diagnosis and management discussed.

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Authors and Affiliations

  1. Ludwig Boltzmann Institute of Osteology at the Hanusch Hospital of WGKK and AUVA Trauma Centre Meidling, 1st Medical Department, Hanusch Hospital, Heinrich-Collin-Straße 30, 1140, Vienna, Austria

    Eva Rath, Klaus Klaushofer & Jochen Zwerina

  2. Institute of Radiology and Nuclear Medicine, Hanusch Hospital, Vienna, Austria

    Shahin Zandieh

  3. Institute of Anesthesiology, Hanusch Hospital, Vienna, Austria

    Alexander Löckinger

  4. Department of Angiology, Hanusch Hospital, Vienna, Austria

    Mirko Hirschl

Authors
  1. Eva Rath
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  2. Shahin Zandieh
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  3. Alexander Löckinger
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  4. Mirko Hirschl
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  5. Klaus Klaushofer
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  6. Jochen Zwerina
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Correspondence to Eva Rath.

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Rath, E., Zandieh, S., Löckinger, A. et al. Life-threatening acute pneumonitis in mixed connective tissue disease: a case report and literature review. Wien Klin Wochenschr 127, 792–794 (2015). https://doi.org/10.1007/s00508-015-0823-6

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  • DOI: https://doi.org/10.1007/s00508-015-0823-6

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