Zusammenfassung
Wir berichten radiologische und klinische Details einer Patientin mit einer durch Syringomyelie und Chiari Typ 1 Malformation ausgelösten neuropathischen Gelenkserkrankung der Schulter. Neuropathische Gelenke sind 1868 erstmals von Charcot beschrieben worden. In der Folge wurden sie bei vielen Arten von peripheren und zentralen Nervenerkrankungen beobachtet. Es gibt viele Gründe für eine Syringomyelie – einer davon ist die Chiari Typ 1 Malformation. Schulter und Ellbogen sind am häufigsten von der Syringomyelie-induzierten Neuropathie befallen. Unsere Patientin wurde 6 Jahre seit der Diagnosestellung einer neuropathischen Arthropathie verbunden mit einer durch Chiari Typ 1 Malformation induzierten Syringomyelie kontrolliert. Nach der Operation zeigte sie keinerlei Progression der Erkrankung.
Summary
We are presenting a case report of neuropathic arthropathy of the shoulder secondary to a syringomyelia and Chiari type I malformation, with detailed clinical and radiological findings. Neuropathic joints were first described in 1868 by Charcot, and subsequently were described in many types of peripheral diseases and central neuron diseases. There are many causes of syringomyelia, and one of the causes of this disease is a Chiari type I malformation. Subsequently, shoulders and elbows are most commonly affected by syringomyelia-induced neuropathy. Our patient was observed for six years after being diagnosed with neuropathic arthropathy and syringomyelia caused by Chiari and did not show any disease progression after their surgery.
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Grahovac, G., Vilendecic, M. & Srdoc, D. Charcot shoulder caused by Chiari type I malformation with syringomyelia with six-year follow-up. Wien Klin Wochenschr 123, 512–514 (2011). https://doi.org/10.1007/s00508-011-0010-3
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DOI: https://doi.org/10.1007/s00508-011-0010-3