Pediatric Nephrology

, Volume 28, Issue 12, pp 2255–2265 | Cite as

The blind kidney: disorders affecting kidneys and eyes

  • Isabelle Russell-Eggitt
  • Detlef Bockenhauer
Educational Review


There are many disorders that can affect both the kidneys and the eyes. Awareness of the ocular manifestations of kidney disorders is important as it can guide the diagnosis and facilitate the choice of a specific treatment. Conversely, ophthalmologists need to be aware of potential renal manifestations in disorders presenting initially with visual failure. We review disorders affecting both of these organ systems, based upon cases from our clinical practice to highlight the importance of interdisciplinary collaboration.


Kidney Eye Children Syndrome 



Case 4 scenario is based upon a case of Professor Christopher Lyons, paediatric ophthalmologist at British Columbia Childrens Hospital, Burnaby, B.C., Canada, who kindly also provided illustration Fig 2f.


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Copyright information

© IPNA 2013

Authors and Affiliations

  1. 1.Department of OphthalmologyGreat Ormond Street Hospital for Children NHS Foundation Trust London UK and UCL Institute of Child HealthLondonUK
  2. 2.Department of NephrologyGreat Ormond Street Hospital for Children NHS Foundation Trust London UK and UCL Institute of Child HealthLondonUK

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