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Renovascular hypertension complicated with VATER association

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Abstract

We report herein a case of a girl with renovascular hypertension associated with VATER association. Her plasma renin activity and aldosterone were high. The ultrasonic echogram and renogram revealed a right hypoplastic kidney without function and a normal-sized left kidney with normal function. Renal angiography revealed a small diameter right main renal artery and a normal left main renal artery with segmental stenosis of left branching renal arteries in the middle segment. Selective renal vein sampling indicated that renin secretion was primarily from the left kidney. This is the first report of renovascular hypertension complicated with VATER association.

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Acknowledgements

The authors are grateful to Dr. Mari Miyazawa, Department of Pediatrics, Kochi Municipal Central Hospital, for her support.

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Authors and Affiliations

  1. Department of Nephrology, National Children’s Medical Center, National Center for Child Health and Development, 10-1 Okura 2-chome Setagaya-ku, 157–8535, Tokyo, Japan

    Jun Inatomi, Rika Fujimaru & Kazumoto Iijima

  2. Department of Radiology, National Children’s Medical Center, National Center for Child Health and Development, Tokyo, Japan

    Osamu Miyazaki

  3. Department of Pediatrics, Faculty of Medicine, The University of Tokyo, 7–3-1 Hongo, Bunkyo-ku, 112-8688, Tokyo, Japan

    Jun Inatomi

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  1. Jun Inatomi
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  2. Osamu Miyazaki
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  3. Rika Fujimaru
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  4. Kazumoto Iijima
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Correspondence to Kazumoto Iijima.

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Inatomi, J., Miyazaki, O., Fujimaru, R. et al. Renovascular hypertension complicated with VATER association. Pediatr Nephrol 20, 1174–1176 (2005). https://doi.org/10.1007/s00467-005-1917-6

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  • DOI: https://doi.org/10.1007/s00467-005-1917-6

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