Abstract
Hemophagocytic syndrome (HPS) is an unusual but severe illness associated with a variety of infections, as well as genetic, malignant tumors, and autoimmune diseases. We report an 11-year-old girl with systemic lupus erythematosus and nephritis who developed HPS associated with Epstein-Barr virus reactivation. In our patient, the onset of reactive HPS might be related to immunosuppressive treatment during the course of lupus nephritis.
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Isome, M., Suzuki, J., Takahashi, A. et al. Epstein-Barr virus-associated hemophagocytic syndrome in a patient with lupus nephritis. Pediatr Nephrol 20, 226–228 (2005). https://doi.org/10.1007/s00467-004-1704-9
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DOI: https://doi.org/10.1007/s00467-004-1704-9