Perspectives on diagnosis and management of adult idiopathic intracranial hypertension

  • Irini Chatziralli
  • Panagiotis Theodossiadis
  • George Theodossiadis
  • Ioannis Asproudis
Review Article



The purpose of this review is to shed light into the diagnostic challenges regarding idiopathic intracranial hypertension (IIH), giving more emphasis to the role of optical coherence tomography (OCT) in IIH, while it also presents recent advances in the management of IIH.


A literature search in PubMed was performed for studies about the diagnosis and management of IIH published before June 30, 2017. Then, a comprehensive review of the eligible studies and the relevant references was performed.


Apart from the updated modified criteria, OCT has been found to be important for the diagnosis of IIH, along with assessment of clinical signs and symptoms, brain imaging, and lumbar puncture. On the other hand, there is no current consensus for the management of IIH, but various interventions have been used, such as dietary therapy (weight loss, bariatric surgery, lifestyle modification, low-salt diet), medications, and surgical treatment.


IIH is a challenging and serious disorder, which may lead to permanent visual impairment if there is a delay in its diagnosis. Advances in retinal imaging have led to better understanding of the pathogenesis of the disease and prompt diagnosis even in subtle cases can be done using OCT. Surgical interventions should be minimized and only used in cases refractory to medical treatment and in those with rapid progression.


Idiopathic intracranial hypertension Pathogenesis Diagnosis Treatment 


Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Ethical approval

This article does not contain any studies with human participants or animals performed by any of the authors.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  • Irini Chatziralli
    • 1
  • Panagiotis Theodossiadis
    • 1
  • George Theodossiadis
    • 1
  • Ioannis Asproudis
    • 2
  1. 1.2nd Department of Ophthalmology, Attikon HospitalUniversity of AthensAthensGreece
  2. 2.Department of OphthalmologyUniversity of IoanninaIoanninaGreece

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