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Application of the new SMS system of cochleovestibular anomalies: our experience with nine cases of type III anomaly

  • Otology
  • Published:
European Archives of Oto-Rhino-Laryngology Aims and scope Submit manuscript

A Letter to the Editor to this article was published on 13 January 2021

Abstract

Objective

To present and analyse the radiological findings, surgical findings, pre-implantation and post-implantation speech and hearing outcomes of nine children with SMS Type III cochleovestibular malformation.

Study design

Retrospective case series of nine children with pre-lingual profound sensorineural hearing loss who underwent cochlear implantation (Jan 2012 to July 2019). These children had been classified as Type III malformation according to the SMS Classification of cochleovestibular anomalies. Facial nerve anomalies, CSF leaks and any other significant surgical finding were noted. Meaningful Auditory Integration Scale (MAIS) was used to report the child’s pre-operative and two-year post-implantation auditory and speech abilities. Any significant improvement was assessed using the Wilcoxon signed rank test. P value < 0.05 was considered significant.

Results

Out of nine patients, five patients sustained CSF gushers, while three patients had mild CSF leak, which were plugged adequately. No facial nerve anomalies were encountered. Post-op course was uneventful for all nine patients. MAIS scores at a two-year follow-up showed significant statistical improvement (P < 0.05) when compared to pre-operative scores.

Conclusion

Cochlear implant is the treatment of choice for children with type III cochleovestibular malformation. There are significant auditory and speech improvements expected. However, the surgeon should bear in mind the risk of CSF leak and subsequent meningitis.

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Funding

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Authors and Affiliations

  1. Department of ENT and Head and Neck Surgery, SMS Medical College and Hospital, Jaipur, Rajasthan, India

    Mohnish Grover & Sunil Samdani

  2. Department of ENT and Head and Neck Surgery, All India Institute of Medical Sciences, New Delhi, India

    Anupam Kanodia

  3. Department of ENT and Head and Neck Surgery, Sardar Patel Medical College, Bikaner, Rajasthan, India

    Gaurav Gupta

  4. Department of ENT and Head and Neck Surgery, All India Institute of Medical Sciences, Bhubaneshwar, India

    Chappity Preetam

Authors
  1. Mohnish Grover
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  2. Anupam Kanodia
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  3. Gaurav Gupta
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  4. Chappity Preetam
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  5. Sunil Samdani
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Contributions

All authors contributed to the study conception and design. Material preparation, data collection and analysis were performed by MG and AK. The first draft of the manuscript was written by AK and all authors commented on previous versions of the manuscript. All authors read and approved the final manuscript.

Corresponding author

Correspondence to Anupam Kanodia.

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Conflict of interest

The authors declare that they have no conflict of interest.

Ethics approval

Ethics approval was not required as it was a retrospective case series and the intervention performed  is part of the routine care.

Informed consent

A written informed consent was obtained from the parents of the children who participated in this study. A written informed consent was obtained from the parents of the children whose data has been published.

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Grover, M., Kanodia, A., Gupta, G. et al. Application of the new SMS system of cochleovestibular anomalies: our experience with nine cases of type III anomaly. Eur Arch Otorhinolaryngol 278, 659–664 (2021). https://doi.org/10.1007/s00405-020-06114-4

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  • DOI: https://doi.org/10.1007/s00405-020-06114-4

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