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Cochlear implantation in an adult patient with auditory neuropathy

  • Audiology
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European Archives of Oto-Rhino-Laryngology and Head & Neck Aims and scope Submit manuscript

Abstract

We present a case report of effective cochlear implantation for an adult patient with auditory neuropathy. A 34-year-old man developed bilateral hearing loss at approximately 10 years of age. His speech discrimination score was very severe despite only moderate sensorineural hearing loss. Absence of auditory brainstem responses (ABR) and preservation of distortion product otoacoustic emissions (DPOAE) were confirmed by our audiological examinations. After cochlear implantation, good responses for electrically evoked compound action potential (EAP) and electrically evoked ABR (EABR) were observed. Postoperatively, his audiological performance was significantly improved. We conclude that cochlear implantation can be a valid option for patients with auditory neuropathy.

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Acknowledgements

We express our sincere thanks to Dr. Jeremy D. Vos of the Vanderbilt University Medical Center for critical review of the final version of this manuscript.

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Authors and Affiliations

  1. Department of Otolaryngology - Head and Neck Surgery, Asahikawa Medical College, Midorigaoka Higashi 2-1-1-1, 078-8510, Asahikawa, Japan

    Akihiro Katada, Satoshi Nonaka & Yasuaki Harabuchi

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  1. Akihiro Katada
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  2. Satoshi Nonaka
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  3. Yasuaki Harabuchi
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Correspondence to Akihiro Katada.

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Katada, A., Nonaka, S. & Harabuchi, Y. Cochlear implantation in an adult patient with auditory neuropathy. Eur Arch Otorhinolaryngol 262, 449–452 (2005). https://doi.org/10.1007/s00405-004-0863-4

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  • DOI: https://doi.org/10.1007/s00405-004-0863-4

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