Zusammenfassung
Das Konzept der IgG4-assoziierten Erkrankungen (IgG4RD) sollte dem Rheumatologen vertraut sein. IgG4RD können durch ihre Symptomatik direkt das Arbeitsgebiet der Rheumatologen betreffen und werden nicht selten primär von diesen diagnostiziert. Darüber hinaus sind sie für eine Vielzahl anderer rheumatischer Erkrankungen eine wichtige Differenzialdiagnose. Auch bei nicht im engeren Sinne den IgG4RD zugehörigen rheumatischen Erkrankungen finden sich zunehmend Beobachtungen, die eine Rolle der mit dem IgG4 verbundenen immunologischen Prozess nahelegen.
Abstract
Rheumatologist should be familiar with the concept of IgG4-related disease (IgG4-RD). Due to the clinical spectrum IgG4-RD can fall directly within the scope of rheumatology and are often diagnosed primarily by rheumatologists. Furthermore, IgG4RD are relevant differential diagnoses for many other rheumatic conditions. Finally, there are an increasing amount of data suggesting an important role of immunological processes observed in IgG4-RD for other rheumatic diseases.
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F. Moosig, J.H. Schirmer, P. Lamprecht und J.U. Holle geben an, dass kein Interessenkonflikt besteht.
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P. Lamprecht, Lübeck
F. Moosig, Neumünster
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Moosig, F., Schirmer, J.H., Lamprecht, P. et al. Klinisches Spektrum der IgG-4-assoziierten Erkrankungen und der Bezug zur Rheumatologie. Z Rheumatol 75, 675–680 (2016). https://doi.org/10.1007/s00393-016-0138-7
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DOI: https://doi.org/10.1007/s00393-016-0138-7