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Klinisches Spektrum der IgG-4-assoziierten Erkrankungen und der Bezug zur Rheumatologie

Clinical spectrum of IgG4-related diseases and the connection to rheumatology

Zeitschrift für Rheumatologie volume 75, pages 675–680 (2016)Cite this article

Zusammenfassung

Das Konzept der IgG4-assoziierten Erkrankungen (IgG4RD) sollte dem Rheumatologen vertraut sein. IgG4RD können durch ihre Symptomatik direkt das Arbeitsgebiet der Rheumatologen betreffen und werden nicht selten primär von diesen diagnostiziert. Darüber hinaus sind sie für eine Vielzahl anderer rheumatischer Erkrankungen eine wichtige Differenzialdiagnose. Auch bei nicht im engeren Sinne den IgG4RD zugehörigen rheumatischen Erkrankungen finden sich zunehmend Beobachtungen, die eine Rolle der mit dem IgG4 verbundenen immunologischen Prozess nahelegen.

Abstract

Rheumatologist should be familiar with the concept of IgG4-related disease (IgG4-RD). Due to the clinical spectrum IgG4-RD can fall directly within the scope of rheumatology and are often diagnosed primarily by rheumatologists. Furthermore, IgG4RD are relevant differential diagnoses for many other rheumatic conditions. Finally, there are an increasing amount of data suggesting an important role of immunological processes observed in IgG4-RD for other rheumatic diseases.

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Affiliations

  1. Rheumazentrum Schleswig-Holstein Mitte, Kuhberg 5a–7, 24534, Neumünster, Deutschland

    F. Moosig & J. U. Holle

  2. 1. Medizinische Universitätsklinik der Christian-Albrechts-Universität zu Kiel, Schittenhelmstr., 24105, Kiel, Deutschland

    J. H. Schirmer

  3. Klinik für Rheumatologie, Universität zu Lübeck, Ratzeburger Allee 160, 23538, Lübeck, Deutschland

    P. Lamprecht

Authors
  1. F. Moosig
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  2. J. H. Schirmer
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  3. P. Lamprecht
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  4. J. U. Holle
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Correspondence to F. Moosig.

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Interessenkonflikt

F. Moosig, J.H. Schirmer, P. Lamprecht und J.U. Holle geben an, dass kein Interessenkonflikt besteht.

Dieser Beitrag beinhaltet keine von den Autoren durchgeführten Studien an Menschen oder Tieren.

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P. Lamprecht, Lübeck

F. Moosig, Neumünster

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Moosig, F., Schirmer, J.H., Lamprecht, P. et al. Klinisches Spektrum der IgG-4-assoziierten Erkrankungen und der Bezug zur Rheumatologie. Z Rheumatol 75, 675–680 (2016). https://doi.org/10.1007/s00393-016-0138-7

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  • DOI: https://doi.org/10.1007/s00393-016-0138-7

Schlüsselwörter

  • Plasmazellen
  • Fibrose
  • Periaortitis
  • Rheumatoide Arthritis
  • Differenzialdiagnose

Keywords

  • Plasma cells
  • Fibrosis
  • Periaortitis
  • Rheumatoid arthritis
  • Differential diagnosis