Zusammenfassung
Die systemische Sklerodermie (SSc) ist eine immunologisch vermittelte entzündliche Bindegewebskrankheit der Haut und zahlreicher extrakutaner Organe, die zu einer ausgedehnten Vaskulopathie kleiner Gefäße und progressiver Fibrose führt. Eine oft wenig beachtete Organmanifestation stellt das Knochengewebe dar. Wir berichten über eine Patientin mit diffuser SSc, bei der es 4 Jahre nach Diagnosestellung der Sklerodermie zu therapieresistenten Schmerzen im Hüftbereich rechts kam. Schmerzursache war eine nichttraumatische Osteonekrose des Caput femoris, die erst mittels MRT diagnostiziert werden konnte.
Abstract
Systemic sclerosis (SSc) is an immune-mediated inflammatory disease of connective tissue that leads to widespread small vessel damage, progressive fibrosis of the skin and numerous extracutaneous organs. An often forgotten manifestation of SSc is in bone. We report on a case of SSc where the patient suffered from unexplainable coxalgia that had started 4 years after the diagnosis of SSc was made. Nontraumatic osteonecrosis of the femoral head was identified by magnetic resonance imaging (MRI) as the underlying cause of the hip pain.
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Buslau, M., Spitzenberger, D. Unklare Hüftschmerzen bei systemischer Sklerodermie. Z. Rheumatol. 72, 601–605 (2013). https://doi.org/10.1007/s00393-013-1152-7
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DOI: https://doi.org/10.1007/s00393-013-1152-7