Zusammenfassung.
Wir berichten über einen 7 Jahre alten Patienten mit totaler cavo-pulmonaler Anastomose mittels extrakardialem Conduit. Zum Zeitpunkt der Operation wurde eine atypische Fenestration angelegt, die das rechte Herzohr mit dem extrakardialen Conduit verband. Eine signifikante arterielle Hypoxämie durch den Rechts-Links-Shunt konnte durch eine modifizierte Implantationstechnik eines 15 mm Helex Schirmsystems erfolgreich behandelt werden.
Summary.
We report on a 7-years old patient after total cavopulmonary anastomosis with an extracardiac conduit. An atypical fenestration was created during the operation connecting the right atrial appendage to the extracardiac conduit. Because of arterial desaturation, the fenestration connecting the anterior wall of the extracardiac conduit to the posterior wall of the right atrial appendage was successfully occluded with a 15 mm Helex device by use of a modified implantation technique.
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Peuster, M., Beerbaum, P. A novel implantation technique for closure of an atypical fenestration connecting the right atrial appendage to an extracardiac conduit by use of a 15 mm Helex device in a patient with total cavopulmonary connection. Z Kardiol 93, 818–823 (2004). https://doi.org/10.1007/s00392-004-0127-8
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DOI: https://doi.org/10.1007/s00392-004-0127-8