Pediatric Surgery International

, Volume 34, Issue 1, pp 109–112 | Cite as

Extraspinal sacrococcygeal ependymoma masquerading as sacrococcygeal teratoma in the pediatric patient

  • Ruchi AminEmail author
  • Elizabeth Berdan
  • Jeffrey Knipstein
  • Jason Jarzembowski
  • Sabina Siddiqui
Case Report


Ependymoma is a glial cell tumor that arises from the ependymal lining of the central nervous ventricular system [1]. These tumors are most commonly seen in children and account for 10% of all central nervous system tumors [1, 2]. There have been rare cases of extraspinal sacrococcygeal ependymomas reported in the literature. These tumors are thought to originate from a group of heterotopic ependymal cells called the coccygeal medullary vestige [3]. While these tumors are often initially misdiagnosed as pilonidal disease, the differential diagnosis also includes congenital tumors such as chordoma, teratoma, and dermoid cysts. This case describes the presentation of an extradural sacrococcygeal subcutaneous ependymoma misdiagnosed as a sacrococcygeal teratoma.

Case presentation

An 8-year-old girl presented to our Pediatric General Surgery Clinic with a several month history of a painful, enlarging soft tissue mass over the coccyx. She had been treated for pilonidal disease...


Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Human and animal rights statement

This article does not contain any studies with human participants performed by any of the authors.

Informed consent

Informed consent was obtained from all individual participants included in the study.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2017

Authors and Affiliations

  1. 1.Pediatric SurgeryMedical College of WisconsinMilwaukeeUSA
  2. 2.Pediatric NeurologyMedical College of WisconsinMilwaukeeUSA
  3. 3.Pediatric PathologyMedical College of WisconsinMilwaukeeUSA

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